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| Case three: Stargardt's disease (Fundus Flavimaculatus) or Juvenile Macular Degeneration |
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 Color fundus photos reveal a beaten bronze appearance in the macula, RPE atrophy and yellow flecks in the posterior pole. |
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 Digital red free photos reveal better visualization of the yellow flecks. |
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 Digital fluorescein angiograms with a hallmark "Dark choroid" and hyperfluorescent flecks in the posterior pole. |
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 Digital ICG angiograms reveal a striking picture of hypo fluorescence of the flecks and atrophic macular changes. |
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Comments |
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| Stargardt's Disease (Fundus Flavimaculatus) or Juvenile Macular Degeneration, is thought to be an autosomal recessive disorder. Visual loss often begins in the first or second decade of life. A beaten bronze metal appearance in the central macula and yellow peripheral flecks along with a "dark" or "silent" choroid on fluorescein angiography are the hallmarks of this disease. Our patient, a 38 year old male, was referred for evaluation of decreased visual acuity of 1 to 1-1/2 years duration. On examination his VA was 20/50 OD and 20/200 OS. Family history was significant for a brother, age 40, who had decreased vision since age 10 which had been described as Juvenile macular degeneration. | |
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Photo credit: , Director of Photography/Webmaster- Southeastern Eye Center |
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