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Central Carolina Surgical Eye Associates, P.A.


Case three: Stargardt's disease
(Fundus Flavimaculatus) or Juvenile Macular Degeneration

Color fundus photos reveal a beaten bronze appearance in the macula, RPE atrophy and yellow flecks in the posterior pole.
Digital red free photos reveal better visualization of the yellow flecks.
Digital fluorescein angiograms with a hallmark "Dark choroid" and hyperfluorescent flecks in the posterior pole.
Digital ICG angiograms reveal a striking picture of hypo fluorescence of the flecks and atrophic macular changes.

Comments

Stargardt's Disease (Fundus Flavimaculatus) or Juvenile Macular Degeneration, is thought to be an autosomal recessive disorder. Visual loss often begins in the first or second decade of life. A beaten bronze metal appearance in the central macula and yellow peripheral flecks along with a "dark" or "silent" choroid on fluorescein angiography are the hallmarks of this disease. Our patient, a 38 year old male, was referred for evaluation of decreased visual acuity of 1 to 1-1/2 years duration. On examination his VA was 20/50 OD and 20/200 OS. Family history was significant for a brother, age 40, who had decreased vision since age 10 which had been described as Juvenile macular degeneration.

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